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Mahaim Syndrome

Mahaim syndrome

Accessory Pathways

Pre-excitation syndrome, James bundle, Lown-Ganog-Levine (LGL) syndrome
  • Physiologically, the atria and ventricles are electrically isolated
    • The only electrical connection is the AV junction
    • If the AV junction is interrupted, a third-degree AV block occurs (electrical isolation of the atria from the ventricles)
  • 0.5% of the population has an additional accessory pathway besides the AV junction
    • The atria and ventricles are electrically connected through two pathways:
      • AV junction
      • Accessory pathway
    • 10% of patients with an accessory pathway also have a secondary accessory pathway
      • which is often inactive
  • Based on location, there are three primary accessory pathways:
    • Kent bundle
      • Connects the atria and ventricles
      • (Atrio-Ventricular bypass)
      • Creates WPW syndrome

    • James bundle
      • Connects the atria to the His bundle
      • (Atrio-Hisian bypass)
      • Creates LGL syndrome

    • Mahaim bundle
      • Connects the AV junction to the ventricles
      • (Nodo-Ventricular bypass)
      • Creates Mahaim syndrome

Mahaim Syndrome

Mahaim fiber, Mahaim syndrome

ECG and Mahaim Syndrome

ECG Mahaim delta wave, normal PR interval

Mahaim fiber, Mahaim syndrome
ECG Mahaim type preexcitation syndrome, normal PR interval, Long QRS, Delta Wave

Mahaim Syndrome




Sources

  • ECG from Basics to Essentials Step by Step
  • litfl.com
  • ecgwaves.com
  • metealpaslan.com
  • medmastery.com
  • uptodate.com
  • ecgpedia.org
  • wikipedia.org
  • Strong Medicine
  • Understanding Pacemakers





šípka späť

Mahaim Syndrome

Mahaim syndrome

Accessory Pathways

  • Physiologically, the atria and ventricles are electrically isolated
    • The only electrical connection is the AV junction
    • If the AV junction is interrupted, a third-degree AV block occurs (electrical isolation of the atria from the ventricles)
  • 0.5% of the population has an additional accessory pathway besides the AV junction
    • The atria and ventricles are electrically connected through two pathways:
      • AV junction
      • Accessory pathway
    • 10% of patients with an accessory pathway also have a secondary accessory pathway
      • which is often inactive
  • Based on location, there are three primary accessory pathways:
    • Kent bundle
      • Connects the atria and ventricles
      • (Atrio-Ventricular bypass)
      • Creates WPW syndrome

    • James bundle
      • Connects the atria to the His bundle
      • (Atrio-Hisian bypass)
      • Creates LGL syndrome

    • Mahaim bundle
      • Connects the AV junction to the ventricles
      • (Nodo-Ventricular bypass)
      • Creates Mahaim syndrome


Pre-excitation syndrome, James bundle, Lown-Ganog-Levine (LGL) syndrome

Mahaim Syndrome

  • Mahaim bundle
    • Connects the AV junction to the ventricles (Nodo-Ventricular bypass)
    • Does not slow down impulse conduction like the AV node
  • PQ interval is normal (0.12 - 0.20s)
    • Impulse slows down in the AV node and then continues
  • Formation of a Delta wave
    • The ventricles are activated earlier via the Mahaim bundle
    • than through the Tawara branches


Mahaim fiber, Mahaim syndrome

ECG and Mahaim Syndrome

ECG Mahaim delta wave, normal PR interval

ECG Mahaim type preexcitation syndrome, normal PR interval, Long QRS, Delta Wave

Mahaim Syndrome

Mahaim fiber, Mahaim syndrome



Sources

  • ECG from Basics to Essentials Step by Step
  • litfl.com
  • ecgwaves.com
  • metealpaslan.com
  • medmastery.com
  • uptodate.com
  • ecgpedia.org
  • wikipedia.org
  • Strong Medicine
  • Understanding Pacemakers